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Von Hippel-Lindau syndrome (VHL) is characterized by an increased risk of developing the tumors listed below:
Hemangioblastomas (benign, or noncancerous, tumors made up of nests of blood vessels) of the brain and spine
Hemangioblastomas of the retina
Pheochromocytomas (a tumor of the chromaffin cells, which are present in the adrenal gland; usually benign, or noncancerous) within or outside of the adrenal gland
Renal cell carcinoma (cancerous tumor of the kidney)
Less commonly, some individuals develop endolymphatic sac tumors (ear tumors that can cause deafness if undetected), pancreatic tumors, and cystadenomas of the epididymis or broad ligament. Other manifestations include cysts (pockets of fluid) of the kidney and pancreas.
The Stanford Medicine Online Second Opinion program offers you easy access to our world-class doctors. It’s all done remotely and you don’t have to visit our hospital or one of our clinics for this service. You don’t even need to leave home!