Complete atresia of coronary ostia in pulmonary atresia and intact ventricular septum PEDIATRIC CARDIOLOGY Selamet, S. E., Hsu, D. T., Thaker, H. M., Gersony, W. M. 2004; 25 (1): 67-69

Abstract

We describe the clinical course, echocardiography, angiography, and histopathology of a female infant with pulmonary atresia and intact ventricular septum (PA/IVS) with complete coronary ostial atresia and right ventricle-dependent coronary circulation who survived for 7 weeks after palliative surgery. The patient expired from myocardial insufficiency while waiting for a donor heart. Postmortem examination demonstrated atretic coronary ostia, ventricular sinusoids, and myocardial infarctions of various ages. This report suggests that neonates with PA/IVS who have this extreme form of coronary abnormality may potentially be managed medically and surgically until cardiac transplantation is available.

View details for DOI 10.1007/s00246-003-0517-0

View details for Web of Science ID 000188455300016

View details for PubMedID 12947508