Notice: Users may be experiencing issues with displaying some pages on stanfordhealthcare.org. We are working closely with our technical teams to resolve the issue as quickly as possible. Thank you for your patience.
 

Learn about the flu shot, COVID-19 vaccine, and our masking policy »

Stanford Health Care

Erdheim-Chester disease: MR imaging, anatomic, and histopathologic correlation of orbital involvement AMERICAN JOURNAL OF NEURORADIOLOGY de Abreu, M. R., Chung, C. B., Biswal, S., Haghighi, P., Hesselink, J., Resnick, D. 2004; 25 (4): 627-630

Abstract

Erdheim-Chester disease (ECD) is a rare form of histiocytosis of unknown origin characterized by tissue infiltration by lipid-laden histiocytes. Typically, the diaphyseal and metaphyseal portions of the tubular bones are affected, leading to a characteristic radiographic pattern of bone sclerosis. Orbital involvement is not infrequent and is manifested by exophthalmos and periorbital xanthomatous lesions, with associated visual problems. This case report documents imaging and pathologic findings in a patient with ECD with extensive orbital involvement.

View details for Web of Science ID 000221042900023

View details for PubMedID 15090356