Epidural spinal involvement of Erdheim-Chester disease causing myelopathy JOURNAL OF CLINICAL NEUROSCIENCE Hwang, B. Y., Liu, A., Kern, J., Goodwin, C. R., Wolinsky, J. P., Desai, A. 2015; 22 (9): 1532-1536


We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.

View details for DOI 10.1016/j.jocn.2015.04.004

View details for Web of Science ID 000359167600037

View details for PubMedID 26119978