Characterization of Pulmonary Artery Stenoses in Alagille Syndrome - a Medical Record Review

Trial ID or NCT#

NCT01515631

Status

not recruiting iconNOT RECRUITING

Purpose

Patients who have Alagille Syndrome (AGS) also frequently have blockages (or "stenoses") of their pulmonary arteries. Little is known about the degree or variability of these stenoses, or the effect of this disease on the right ventricle (the chamber of the heart which pumps blood to the lungs). This study will first quantify and describe pulmonary artery stenosis in patients with Alagille Syndrome. The study will also assess the effect of these stenoses on the right ventricle. The investigators hope to learn the degree and characteristics of pulmonary artery stenosis in Alagille Syndrome. The investigators also hope to learn the effect of this pulmonary artery stenosis on the right ventricle in patients with Alagille Syndrome. This information is critical in the management of patients with Alagille syndrome, as there is currently no data to guide clinicians on the management of pulmonary artery stenosis. Furthermore, the information from this study may help physicians manage pulmonary artery stenosis in other patients as well.

Official Title

Characterization of Pulmonary Artery Stenoses in Alagille Syndrome - a Medical Record

Eligibility Criteria

Sexes Eligible for Study: All
Accepts Healthy Volunteers: No
Inclusion Criteria:
  1. - Diagnosis of Alagille Syndrome
Exclusion Criteria:
  1. - None

Contact us to find out if this trial is right for you.

Contact

Jeffrey Feinstein, MD, MPH
650 723 7913