Diagnosing Epithelioid Hemangioendothelioma with Pericardial Involvement. The Annals of thoracic surgery Balansay, B. E., Zhang, X., Loftus, P. D., Valenzuela, J. A., Zambrano, E., Lee, A. M. 2018

Abstract

Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor that commonly affects lung, liver, and bone. Among all known EHE cases, only 20% have a pulmonary origin, with metastases to the pericardium occurring in less than 1% of these. Due to its low prevalence, variable presentation, and unknown latency period, a thoracic EHE diagnosis can be easily missed. This case outlines the unique pathologic features of EHE in a patient with cardiovascular disease, provides further insight into diagnosing a rare tumor, and provides a better understanding of the pathophysiology and progression of thoracic EHE.

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